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KMID : 1149520210050030118
Cardiovasclar Imaging Asia
2021 Volume.5 No. 3 p.118 ~ p.119
Unicommisural Unicuspid Aortic Valve with Very Severe Aortic Stenosis in a 17-Year-Old Female
Velamakanni Subrahmanya Murti

Khadkikar Gajanan
Patel Aman
Patel Tejas
Abstract
Unicuspid aortic valve is a rare congenital anomaly associated with early onset of severe aortic stenosis, incompetence, or both. It is frequently misdiagnosed as a bicuspid aortic valve. Here, we present echocardiographic images of a 17-year-old with a unicuspid unicommisural aortic valve who presented with symptomatic severe aortic stenosis with a very high mean transvalvular gradient of 134 mm Hg.
KEYWORD
Aortic valve stenosis, Heart valve disease, Congenital heart defect
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